Zusammenfassung
Die Gallengangsatresie ist eine Erkrankung des Neugeborenenalters, deren frühzeitige
Diagnose entscheidend ist, da nur eine rechtzeitige Operation (Portoenterostomie nach
Kasai) die Kinder vor einer biliären Leberzirrhose bewahren kann. Die hepatobiliäre
Funktionsszintigrafie besitzt eine zentrale Bedeutung in der Diagnostik, in der Prognosebeurteilung
und in der postoperativen Verlaufskontrolle der Gallengangsatresie. Mit diesem Artikel
soll die Indikationsstellung, die Durchführung und die Beurteilung der hepatobiliären
Funktionsszintigrafie bei Neugeborenen mit dem Verdacht auf eine Gallengangsatresie
dargestellt werden.
Abstract
In newborns with biliary atresia immediate diagnosis is crucial, as only early portoenterostomie
(Kasai) may prevent development of an incurable liver cirrhosis. Hepatobiliary scintigraphy
has a major role in diagnostic work up, in prognostic evaluation and in postoperativ
follow up of biliary atresia. Indication, technical procedure and interpretation of
hepatobiliary scintigraphy in children with suspicion of biliary atresia will be discussed.
Schlüsselwörter
Leberfunktionsszintigrafie - Gallengangsatresie - Portoenterostomie
Key words
hepatobiliary scintigraphy - biliary atresia - portoenterostomy
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Korrespondenzadresse
Dr. B. Roßmüller
Email: brossmueller@t-online.de
